Case (reference)
Age (y) Stage Diagnosis Residual tumor
Operation method First-line chemotherapy
Secondary-line chemotherapy
radiotherapy Follow-up (moths)
Clinical outcomes 1
[5]
25 IA PNET NA ATH,BSO No
No No
60 L&W
2 [5]
16 IA PNET NA ATH,BSO No
No No
NA NA
3 [5]
49 IA PNET NA ATH,BSO No
No No
48 L&W
4 [5]
36 IIA PNET NA ATH,BSO No
No No
36 L&W
5 [5]
35 III PNET NA ATH,LSO ? ?
No
60 LWD
6 [5]
30 III PNET NA ATH,BSO,
omentectomy ? ? Yes 60 DOD
7 [5]
24 IA PNET NA USO No No
No
NA NA
8 20 IA PNET NA LSO ? ? 108 L&W
9 [5]
32 IA PNET NA LSO ? ?
No
36 L&W
10 [5]
16 IC PNET NA RSO ? ?
No
7 L&W
11 [5]
13 III PNET NA RSO No No
No
20 DOD
12 [5]
18 III PNET NA RSO No
No
Yes
3 DOD
13 [5]
18 III PNET NA RSO No
No
Yes
7 DOD
14 [5]
18 III PNET NA RSO ? ?
No
6 DOD
15 [5]
26 III PNET NA BSO ? ?
No
1 LWD
16 [5]
69 III PNET NA LSO ? ?
Yes
6 DOD
[5]
23 III PNET NA ATH,BSO ? ?
Yes
2 DOD
18 [5]
16 NA PNET NA NA NA NA NA NA NA
19 [5]
6 IA PNET NA RSO No
No No
24 DOD
20 [5]
17 IA PNET NA LSO No
No No
48 L&W
21 [5]
15 IA PNET NA LO No
No No
36 L&W
22 [5]
16 IIA PNET NA ATH,BSO No
No No
60 DOD
23 [5]
15 IIA PNET NA RSO,LO No
No No
12 LWD
24 [5]
22 IIB PNET NA LSO No No No NA NA
25 22 III PNET NA RO ? ? Yes 4 DOD
26
[8] 18 IIIC PNET Peritoneal
seeding
RSO,omentectomy, LN biopsy
Carboplatin, paclitaxel
Vincristine, actinomycin, cyclophosphamide,
doxorubicin
pelvic cavity
radiotherapy 10 DOD
27 [10]
25 IC PNET
No residual
tumor
LSO, pelvic and para-aortic LN
dissection
Bleomycin,etoposid e,cisplatin * 4
Vincristine,
ifosfamide,cisplatin *6 No
36 L&W
28 [11]
28 IV PNET lung,
adrenal RSO
Doxorubicin, cyclophosphamide,
vincristine
Doxorubicin, actionomycin,clophosp
hamide,vincristine No
13 DOD
29
[12]
31 IIIC PNET Peritoneal
seeding
ATH,BSO,omentect omy
Vincristine, doxorubicin,
ifosfamide alternated with
vincristine, actinomycin, ifosfamide *4
Docetaxel,cisplatin *3
No
15 DOD
30 [13]
28 III PNET
No residual
tumor
LSO, cytoreduction,oment
ectomy
Vincristine, ifosfamide,
etoposide No No
18 DOD
31
[15] 18 IIIC EWS
No residual
tumor
BSO,omentectomy, cytoreduction, enterectomy with
anastomosis
Ifosfamide, epirubicin, dacarbazine *6
No No 10 DOD
[9]
16 IC PNET residual
tumor
dissection,
omentectomy paclitaxel * 6 No No
13 L&W
33
[14] 37 IIIC PNET Peritoneal
seeding
STH,BSO,omentecto my,pelvic LN
dissection, cytoreduction
Etoposide, cisplatin, cyclophosphamide
* 10
Doxorubicin,dacarbazi
ne No 8 LWD
34 [6]
39 III EWS NA ?? ? ?
No
NA L&W
35 [6]
12 I EWS NA ?? No No
No
NA NA
36 [6]
15 IV
EWS
NA ??
No No No
12 L&W
37 [6]
24 III
EWS
NA ??
No No No
NA NA
38 [6]
36 II
EWS
NA ??
No No No
36 L&W
39 [6]
14 III
EWS
NA ??
No No
Yes NA DOD
[6]
18 I NA ??
No No
No NA NA
41 [6]
NA NA
EWS
NA NA NA NA NA NA NA
42 [6]
NA I
EWS
NA NA NA NA NA 12 L&W
43 [6]
16 I EWS NA ?? -
No No
36 L&W
44
(this case)
22 IV PNET
Peritoneal seeding, liverparen
chyma
ATH + BSO + omentectomy +cytoreduction +enterectomy with
anastomosis
Vincristine,doxorub icin, cyclophosphamide,
alternated with ifosfamide,
etoposide
No No
15 DOD
EWS: Ewing sarcoma; PNET: peripheral primitive neuroectodermal tumor,
ATH: abdominal total hysterectomy; BSO: bilateral salpingo-oophorectomy, LN: lymph node; LSO:left salpingo-oophorectomy; RSO:right salpingo-oophorectomy; LO: left oophorectomy; STH: subtotal hysterectomy; NA: not available; ??: unspecified; ?: chemotherapy without detail description; DOD: died of disease; LWD: live with disease; L&W: live without disease