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Appendix. Details of patients presenting with PCV serotypes Year of

presentation Age Sex Underlying risk factor for infection

Prior pneumococcal infection

Infection Vaccination Investigation for

immunodeficiency Underlying cause Serotype

19F

2014 13y 2m

F Yes, dysplastic cochlea predisposing to CSF leak

Yes, 2 prior presentations with meningitis (Serotype 19F and unknown)

Sepsis, meningitis Yes Yes Anatomical

abnormality causing CSF leak. No immunodeficiency found

2015 2m M No No Meningitis,

subdural collection

No Yes No

2015 1y 4m F No No Sepsis Yes No -

2016 7y M No No Sepsis, pneumonia No Yes No

2016 15y

1m M No No Sepsis, pneumonia Yes No -

Serotype 1

2011 1y 4m M No No Pneumonia,

bacteremia

Yes No -

Serotype 7F

2011 3y 7m M No No Sepsis, empyema Yes No -

2011 5y 3m M No No Pneumonia,

bacteremia

Yes No -

2011 6y 3m F No No Pneumonia,

bacteremia

Yes No -

2013 6y 8m M No No Sepsis, meningitis,

mastoiditis Yes No -

2013 1y 5m M No No Pneumonia,

bacteremia

Yes No -

2013 2m M No No Sepsis, meningitis Yes No -

2014 2y 3m M Neuroblastoma No Septic shock, Yes No -

27

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, autologous stem cell transplant

pneumonia

2014 1m M No No Sepsis, meningitis - No -

Serotype 3

2011 1y 3m M No No Pneumonia,

bacteremia Yes No -

2013 2y 5m M No No Sepsis, pneumonia Yes No -

2014 1y 2m M No No Empyema,

necrotizing pneumonia

Yes No -

2016 2y3m M No No Empyema Yes No -

2016 2y

10m

F No No Empyema Yes No -

2016 3y F No No Empyema Yes No -

2016 3y 9m M No No Empyema Yes Yes No

2016 4y 4m F No No Empyema Yes No -

2017 2y 1m M No No Empyema Yes No -

2017 5y

11m M No No Empyema Yes Incomplete No

Serotype 19A

2011 1y 7m M No No Sepsis, pneumonia Yes No -

2011 8m F No No Septic arthritis Yes No -

2011 10m M No No Sepsis, meningitis

with SDC Yes No -

2011 1y 1m M No No Sepsis, meningitis Yes No -

2011 1m M No No Sepsis, meningitis No No -

2011 3y 2m M No No Empyema Yes No -

2011 3m F No No Meningitis No No -

2011 10m M No No Mastoiditis Yes No -

2011 4y 1m F No No Pneumonia,

bacteremia

Yes No -

2012 2y 4m F No No Sepsis, empyema No No -

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2012 4y 4m M No No Empyema Yes No -

2013 7y 2m M Acute

lymphoblastic leukaemia, chemotherapy

No Sepsis Yes No -

2014 3m M No No Sepsis, meningitis

with subdural collection, osteomyelitis

Yes No -

2014 1y

10m

M No No Sepsis, empyema Yes No -

2014 1y F No No Sepsis, empyema Yes No -

Serotype 23F

2016 4y

10m F No No Empyema Yes No -

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