Supplementary Table 1. Pure tone audiometry (left ear), P values for post hoc tests for each
frequency.
Frequency Fabry vs. Diabetic Fabry vs. control Diabetic vs. control
125 Hz 0.556 <0.001 <0.001
250 Hz 1.000 0.001 0.001
500 Hz 0.227 0.053 <0.001
1000 Hz 0.224 0.649 0.012
2000 Hz 0.006 1.000 0.020
4000 Hz 0.208 0.032 <0.001
6000 Hz 0.062 0.001 <0.001
8000 Hz 0.001 0.925 <0.001
9000 Hz 0.014 <0.001 <0.001
10 kHz 0.039 <0.001 <0.001
12 kHz 0.026 <0.001 <0.001
14 kHz 0.013 <0.001 <0.001
16 kHz 0.025 <0.001 <0.001
Supplementary Table 2. Pure tone audiometry (right ear), P values for post hoc tests for each
frequency.
Frequency Fabry vs. Diabetic Fabry vs. control Diabetic vs. control
125 Hz 0.482 0.016 <0.001
250 Hz 0.932 0.005 <0.001
500 Hz 0.078 0.299 0.001
1000 Hz 0.075 1.000 0.020
2000 Hz NA
4000 Hz 0.086 1.000 0.009
6000 Hz 0.654 <0.001 <0.001
8000 Hz 0.170 1.000 0.018
9000 Hz 0.205 <0.001 <0.001
10 kHz 0.074 0.001 <0.001
12 kHz 0.006 <0.001 <0.001
14 kHz 0.001 <0.001 <0.001
16 kHz 0.006 <0.001 <0.001
NA: Not applicable
Supplementary Table 3. Distortion product otoacoustic emission (left ear), P values for post
hoc tests for each frequency.
Frequency Fabry vs. Diabetic Fabry vs. control Diabetic vs. control
504 Hz NA
598 Hz NA
703 Hz 0.073 1.000 0.088
844 Hz NA
996 Hz NA
1184 Hz NA
1418 Hz 0.130 1.000 0.029
1688 Hz 0.012 1.000 0.012
2004 Hz 0.017 1.000 0.008
2379 Hz 0.038 1.000 0.023
2824 Hz 0.001 1.000 <0.001
3363 Hz 0.020 0.284 <0.001
3996 Hz 0.013 0.673 <0.001
4758 Hz 0.050 0.881 0.002
5660 Hz 0.222 0.748 0.013
6727 Hz 0.081 1.000 0.028
8004 Hz NA
9516 Hz NA
11309 Hz NA
NA: Not applicable
Supplementary Table 4. Distortion product otoacoustic emission (right ear), P values for
post hoc tests for each frequency.
Frequency Fabry vs. Diabetic Fabry vs. control Diabetic vs. control
504 Hz NA
598 Hz NA
703 Hz NA
844 Hz 0.035 1.000 0.135
996 Hz 0.109 1.000 0.024
1184 Hz 0.168 1.000 0.029
1418 Hz 0.062 0.999 0.004
1688 Hz 0.003 1.000 <0.001
2004 Hz 0.001 0.401 <0.001
2379 Hz 0.004 1.000 0.002
2824 Hz 0.015 1.000 0.002
3363 Hz 0.019 0.047 <0.001
3996 Hz 0.009 0.015 <0.001
4758 Hz 0.012 0.056 <0.001
5660 Hz 0.031 0.842 <0.001
6727 Hz 0.017 1.000 0.030
8004 Hz 0.006 1.000 0.037
9516 Hz 0.050 1.000 0.091
11309 Hz 0.048 1.000 0.056
NA: Not applicable